Study of the deficit in planning abilities of adults with Prader-Willi Syndrome
Language
EN
Article de revue
This item was published in
Research in Developmental Disabilities. 2021-10-21, vol. 117, p. 104056
English Abstract
Background: Prader-Willi syndrome (PWS) is a complex developmental genetic disorder associated
with intellectual disability and deficits in executive functions which result in disorganisation
and poor personal autonomy.
Aims: ...Read more >
Background: Prader-Willi syndrome (PWS) is a complex developmental genetic disorder associated
with intellectual disability and deficits in executive functions which result in disorganisation
and poor personal autonomy.
Aims: This study aimed to determine impairments in planning skills of adults with PWS, in
relation with their intellectual disabilities, as well as the influence of food compulsions on their
performance.
Methods and procedures: A modified version of the Zoo Map from the Behavioural Assessment of
the Dysexecutive Syndrome was used in three groups: a group of adults with PWS in comparison
with two groups both matched on chronological age, one with typical development (TD) and one
with intellectual disability (ID).
Outcomes and results: Compared to TD adults, both adults with PWS and ID showed increased
planning time and lower raw scores on the planning task. The execution time and the number of
errors were higher in the PWS group compared to the comparison groups. All three groups performed
worse in the non-food condition only for number of errors and raw score.
Conclusions and implications: Planning abilities were impaired in PWS adults. Results also showed
that intellectual level plays a role in participants’ performance. These findings are essential to
understand the difficulties of people with PWS daily life.Read less <
English Keywords
Cognitive profile
Intellectual disability
Planning
Prader-Willi Syndrome
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