FIORE, Mathieu; GIRAUDET, Janine-Sophie; ALESSI, Marie-Christine; FALAISE, Céline; DESPREZ, Dominique; D'OIRON, Roseline; VOISIN, Sophie; HURTAUD, Marie-Françoise; BOUTROUX, Hélène; SAULTIER, Paul; LAVENU-BOMBLED, Cécile; BAGOU, Gilles; DUBUCS, Xavier; CHAUVIN, Anthony; LEROY, Christophe; MECKERT, Francine; KERBAUL, François; GIRAUD, Nicolas; PÜHLER, Ambra; RATH, Ana

Métadonnées

Afficher la notice complète

Licence d’utilisation du document

FIORE, Mathieu
Biologie des maladies cardiovasculaires = Biology of Cardiovascular Diseases

GIRAUDET, Janine-Sophie

ALESSI, Marie-Christine

Langue

Article de revue

Ce document a été publié dans

Orphanet Journal of Rare Diseases. 2023-06-29, vol. 18, n° 1, p. 171

Résumé en anglais

Glanzmann thrombasthenia (GT) is a genetic bleeding disorder characterised by severely reduced/absent platelet aggregation in response to multiple physiological agonists. The severity of bleeding in GT varies markedly, as does the emergency situations and complications encountered in patients. A number of emergency situations may occur in the context of GT, including spontaneous or provoked bleeding, such as surgery or childbirth. While general management principles apply in each of these settings, specific considerations are essential for the management of GT to avoid escalating minor bleeding events. These recommendations have been developed from a literature review and consensus from experts of the French Network for Inherited Platelet Disorders, the French Society of Emergency Medicine, representatives of patients' associations, and Orphanet to aid decision making and optimise clinical care by non-GT expert health professionals who encounter emergency situations in patients with GT.< Réduire

Mots clés

Article clinique

Mots clés en anglais

Humans

Thrombasthenia

Consensus

Emergency Medicine

Health Personnel

URI

https://oskar-bordeaux.fr/handle/20.500.12278/184364

Unités de recherche

Biologie des maladies cardiovasculaires (BMC) - UMR 1034