Acquired haemophilia A in paediatric patients: A retrospective French cohort of eight cases.
dc.rights.license | open | en_US |
hal.structure.identifier | Laboratory of Hematology, Bordeaux University Hospital, Avenue de Magellan, 33604, Pessac | |
dc.contributor.author | MOUTHON, Paul | |
hal.structure.identifier | Biologie des maladies cardiovasculaires = Biology of Cardiovascular Diseases | |
hal.structure.identifier | Laboratory of Hematology, Bordeaux University Hospital, Avenue de Magellan, 33604, Pessac | |
dc.contributor.author | GUY, Alexandre | |
dc.contributor.author | D'OIRON, Roseline | |
dc.contributor.author | HARROCHE, Annie | |
dc.contributor.author | LEBRETON, Aurélien | |
dc.contributor.author | GOURGUECHON, Clément | |
dc.contributor.author | OUDOT-CHALLARD, Caroline | |
dc.contributor.author | HUGUENIN, Yoann | |
dc.date.accessioned | 2024-03-25T14:31:23Z | |
dc.date.available | 2024-03-25T14:31:23Z | |
dc.date.issued | 2024-02-01 | |
dc.identifier.issn | 1365-2141 | en_US |
dc.identifier.uri | https://oskar-bordeaux.fr/handle/20.500.12278/188960 | |
dc.description.abstractEn | Acquired haemophilia A (AHA) is a rare haemorrhagic disease characterised by new-onset haemorrhagic symptoms associated with a dramatic decrease in factor VIII levels and an anti-factor VIII neutralising autoantibody concentration >0.6 Bethesda units. Elderly people are often affected, whereas children are rarely affected; the paediatric incidence reported in the literature is about 0.045 case/million/year. For some time, the paediatric standard of care has been that for adults, but clinicians have often reported poor outcomes. Here, we describe the largest retrospective paediatric AHA cohort assembled to date, including eight patients diagnosed in France from 2000 to 2020. | |
dc.language.iso | EN | en_US |
dc.rights | Attribution-NonCommercial 3.0 United States | * |
dc.rights.uri | http://creativecommons.org/licenses/by-nc/3.0/us/ | * |
dc.subject.en | Adult | |
dc.subject.en | Humans | |
dc.subject.en | Child | |
dc.subject.en | Aged | |
dc.subject.en | Hemophilia A | |
dc.subject.en | Retrospective Studies | |
dc.subject.en | Hemorrhage | |
dc.subject.en | Autoantibodies | |
dc.subject.en | Factor VIII | |
dc.title.en | Acquired haemophilia A in paediatric patients: A retrospective French cohort of eight cases. | |
dc.title.alternative | Br J Haematol | en_US |
dc.type | Article de revue | en_US |
dc.identifier.doi | 10.1111/bjh.19285 | en_US |
dc.subject.hal | Sciences du Vivant [q-bio]/Médecine humaine et pathologie | en_US |
dc.identifier.pubmed | 38192055 | en_US |
bordeaux.journal | British Journal of Haematology | en_US |
bordeaux.page | 606-611 | en_US |
bordeaux.volume | 204 | en_US |
bordeaux.hal.laboratories | Biologie des maladies cardiovasculaires (BMC) - UMR 1034 | en_US |
bordeaux.issue | 2 | en_US |
bordeaux.institution | Université de Bordeaux | en_US |
bordeaux.institution | INSERM | en_US |
bordeaux.peerReviewed | oui | en_US |
bordeaux.inpress | non | en_US |
bordeaux.import.source | pubmed | |
hal.identifier | hal-04520216 | |
hal.version | 1 | |
hal.date.transferred | 2024-03-25T14:31:25Z | |
hal.popular | non | en_US |
hal.audience | Internationale | en_US |
hal.export | true | |
workflow.import.source | pubmed | |
dc.rights.cc | Pas de Licence CC | en_US |
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