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Emergency management of patients with Glanzmann thrombasthenia: consensus recommendations from the French reference center for inherited platelet disorders.

dc.rights.licenseopenen_US
hal.structure.identifierBiologie des maladies cardiovasculaires = Biology of Cardiovascular Diseases
dc.contributor.authorFIORE, Mathieu
dc.contributor.authorGIRAUDET, Janine-Sophie
dc.contributor.authorALESSI, Marie-Christine
dc.contributor.authorFALAISE, Céline
dc.contributor.authorDESPREZ, Dominique
dc.contributor.authorD'OIRON, Roseline
dc.contributor.authorVOISIN, Sophie
dc.contributor.authorHURTAUD, Marie-Françoise
dc.contributor.authorBOUTROUX, Hélène
dc.contributor.authorSAULTIER, Paul
dc.contributor.authorLAVENU-BOMBLED, Cécile
dc.contributor.authorBAGOU, Gilles
dc.contributor.authorDUBUCS, Xavier
dc.contributor.authorCHAUVIN, Anthony
dc.contributor.authorLEROY, Christophe
dc.contributor.authorMECKERT, Francine
dc.contributor.authorKERBAUL, François
dc.contributor.authorGIRAUD, Nicolas
dc.contributor.authorPÜHLER, Ambra
dc.contributor.authorRATH, Ana
dc.date.accessioned2023-10-09T14:14:27Z
dc.date.available2023-10-09T14:14:27Z
dc.date.issued2023-06-29
dc.identifier.issn1750-1172en_US
dc.identifier.urihttps://oskar-bordeaux.fr/handle/20.500.12278/184364
dc.description.abstractEnGlanzmann thrombasthenia (GT) is a genetic bleeding disorder characterised by severely reduced/absent platelet aggregation in response to multiple physiological agonists. The severity of bleeding in GT varies markedly, as does the emergency situations and complications encountered in patients. A number of emergency situations may occur in the context of GT, including spontaneous or provoked bleeding, such as surgery or childbirth. While general management principles apply in each of these settings, specific considerations are essential for the management of GT to avoid escalating minor bleeding events. These recommendations have been developed from a literature review and consensus from experts of the French Network for Inherited Platelet Disorders, the French Society of Emergency Medicine, representatives of patients' associations, and Orphanet to aid decision making and optimise clinical care by non-GT expert health professionals who encounter emergency situations in patients with GT.
dc.language.isoENen_US
dc.subjectArticle clinique
dc.subject.enHumans
dc.subject.enThrombasthenia
dc.subject.enConsensus
dc.subject.enEmergency Medicine
dc.subject.enHealth Personnel
dc.title.enEmergency management of patients with Glanzmann thrombasthenia: consensus recommendations from the French reference center for inherited platelet disorders.
dc.title.alternativeOrphanet J Rare Disen_US
dc.typeArticle de revueen_US
dc.subject.halSciences du Vivant [q-bio]/Médecine humaine et pathologieen_US
dc.identifier.pubmed37386449en_US
bordeaux.journalOrphanet Journal of Rare Diseasesen_US
bordeaux.page171en_US
bordeaux.volume18en_US
bordeaux.hal.laboratoriesBiologie des maladies cardiovasculaires (BMC) - UMR 1034en_US
bordeaux.issue1en_US
bordeaux.institutionUniversité de Bordeauxen_US
bordeaux.institutionINSERMen_US
bordeaux.peerReviewedouien_US
bordeaux.inpressnonen_US
bordeaux.import.sourcepubmed
hal.identifierhal-04233663
hal.version1
hal.date.transferred2023-10-09T14:14:29Z
hal.popularnonen_US
hal.audienceInternationaleen_US
hal.exporttrue
workflow.import.sourcepubmed
dc.rights.ccPas de Licence CCen_US
bordeaux.COinSctx_ver=Z39.88-2004&rft_val_fmt=info:ofi/fmt:kev:mtx:journal&rft.jtitle=Orphanet%20Journal%20of%20Rare%20Diseases&rft.date=2023-06-29&rft.volume=18&rft.issue=1&rft.spage=171&rft.epage=171&rft.eissn=1750-1172&rft.issn=1750-1172&rft.au=FIORE,%20Mathieu&GIRAUDET,%20Janine-Sophie&ALESSI,%20Marie-Christine&FALAISE,%20C%C3%A9line&DESPREZ,%20Dominique&rft.genre=article


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